Accelerated approval granted for drug developed at GOSH

14 Dec 2016, 9:55 a.m.

Dr Francesco Muntoni appears stood in a laboratiry wearing an olive green tie and a white shirt with shelves of medical equipment and other assorted containers in the background.

The United States Food and Drug Administration (FDA) granted accelerated approval for a new medication to treat Duchenne muscular dystrophy (DMD). The drug, Eteplirsen, was developed by a UK consortium led by Novel Therapies Theme lead, Professor Francesco Muntoni.

DMD is a severe, muscle-wasting condition caused by a fault in a gene, resulting in a failure to produce functional dystrophin. Currently DMD has few treatment options.

Eteplirsen was filed by Sarepta Therapeutics for accelerated approval by the FDA and is planned for immediate clinical use in the US. The approval for use in the EU is still underway. The drug will be used to treat patients with a specific subset of mutations of the dystrophin gene that affects around 13% of boys with DMD.

The drug ‘skips’ a part of the gene that makes dystrophin, which results in a shortened form of the dystrophin protein being produced, alleviating some of the symptoms of DMD and potentially extending a patient's mobility for a longer period of time.

Read the full press release.

Researchers identify brain network linked to deadliest childhood brain cancer

Researchers at GOSH and University College London have identified a human brain network associated with survival in children with diffuse midline glioma, the deadliest childhood brain cancer.

Families and researchers come together for BPAN Family Day

Families affected by BPAN came together with clinicians and researchers at GOSH

Better understanding leukaemia for children with down syndrome

Researchers have mapped the evolution of a type of leukaemia that is exclusive to children with Down syndrome and may have identified an overarching weakness in the cancer's genetic makeup.

‘Ready-made’ T-cell gene therapy tackles ‘incurable’ T-Cell leukaemia

A groundbreaking new treatment using gene-edited immune cells, developed at GOSH and UCL has shown promising results in helping children and adults fight a rare and aggressive cancer