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Cystic fibrosis

This information from Great Ormond Street Hospital is about cystic fibrosis (CF) – an inherited disease primarily affecting the lungs and digestive system. It happens because the gene that is responsible for making mucus is faulty. Normally, the mucus that lines our internal organs is clear, lubricating and protects against infection. In babies with CF, it is thick, congesting and prone to infection. 

Enzymes in cystic fibrosis 

Digestive enzymes are made in the pancreas. The fat, protein and carbohydrate in food is broken down by the enzymes to release nutrients. „„In cystic fibrosis (CF) sticky mucus blocks the passages from the pancreas to the small intestine which stops the enzymes working, so the food cannot be digested or absorbed by the body. This is called malabsorption and causes loose or oily stools, wind, stomach ache and poor weight gain.

Puppy Ward (Test Ward)

Puppy Ward is a 14-bed ward caring for children with a variety of respiratory conditions from cystic fibrosis to empyema/pneumothorax and complex asthma.

We also look after children who require respiratory support from a ventilator (either via a face mask or tracheostomy).

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