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Cystic fibrosis

This information from Great Ormond Street Hospital is about cystic fibrosis (CF) – an inherited disease primarily affecting the lungs and digestive system. It happens because the gene that is responsible for making mucus is faulty. Normally, the mucus that lines our internal organs is clear, lubricating and protects against infection. In babies with CF, it is thick, congesting and prone to infection. 

Cystic fibrosis

Cystic fibrosis (CF) is an inherited disease which mainly affects your lungs and digestive system. It clogs up these organs with thick, sticky mucus which can lead to symptoms like a cough, chest infections and difficulty absorbing and digesting fat in food.

Enzymes in cystic fibrosis 

Digestive enzymes are made in the pancreas. The fat, protein and carbohydrate in food is broken down by the enzymes to release nutrients. „„In cystic fibrosis (CF) sticky mucus blocks the passages from the pancreas to the small intestine which stops the enzymes working, so the food cannot be digested or absorbed by the body. This is called malabsorption and causes loose or oily stools, wind, stomach ache and poor weight gain.